Rhabdomyosarcoma of the soft palate: a diagnostic challenge
Keywords:Children, Diagnosis, Rhabdomyosarcoma, Sarcoma, Soft palate, Surgery
Introduction: Rhabdomyosarcoma (RMS) accounts for 50% of all soft tissue sarcomas in children. 10-30% of head and neck RMS have their origin in intraoral and pharyngeal structures. When these lesions grow rapidly reaching a large dimensions they may cause potencially serious symptoms.
Case Report: A ten-years-old boy presented in Otorynolaryngology emergency department with a fast growing large soft palate lesion, causing dyspneia and dysphagia (previously treated as an inflammatory lesion). He was submitted to a partial excision of the lesion and histologic exam revealed rhabdomyoma. After three months a new fast growth of the lesion was seen. A new excisional biopsy was performed and the extemporaneous pathological examination was compatible with a benign lesion. Definitive diagnosis was rhabdomyosarcoma.
Discussion/Conclusion: The authors illustrate that the diagnosis of RMS can be a challenge and emphasizes the importance of urgent reference and multidisciplinar approach in children with any fast growing lesion.
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