• Aida Silva e Sá Department of Pediatrics, Centro Hospitalar Trás -os -Montes de Alto Douro
  • José Carlos Fraga Department of Pediatrics, Centro Hospitalar Trás -os -Montes de Alto Douro
  • Ana Margarida Costa Department of Pediatrics, Centro Hospitalar Trás -os -Montes de Alto Douro
  • Fátima Dias Department of Rheumatology, Centro Hospitalar São João
  • Iva Brito Department of Rheumatology, Centro Hospitalar São João




Hydroxychloroquine, myositis, recurrent parotitis, Sjögren Syndrome


Introduction: Juvenile recurrent parotiditis (JRP) is a relapsing inflammation of the parotid gland, usually associated with non-obstructive sialectasis. The Sjögren syndrome (SS), rare in children, may present at this age, in the form of recurrent parotiditis.
Case Study: Female, 13 years, in the fourth episode of parotid swelling and pain, begins investigating: ultrasound of the parotid glands revealed heterogeneous texture and multiple punctiforme calcifications, high ANA (1:1280) title, with speckled pattern, auto-antibodies anti-SSA, anti-SSB and Rheumatoid Factor positive, hyper-gamaglobulinemia and elevated Immunoglobulin G. We also observed elevation of Creatinofosfoquinase, Glutamic Oxaloacetic Transaminase and Glutamic Pyruvic Transaminase. A minor salivary gland biopsy was consistent with a diagnosis of SS. Treatment was started with systemic steroids combining hydroxychloroquine during exacerbations, with clinical improvement.
Discussion/conclusion: The age of onset of parotid swelling helps in differentiation between JRP idiopathic and other clinical entities. The muscle involvement occurs in primary SS and has a varied clinical and pathological spectrum, subclinical myositis occurs in a percentage that varies between 5% and 37%.


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How to Cite

e Sá AS, Fraga JC, Costa AM, Dias F, Brito I. JUVENILE RECURRENT PAROTIDITIS…NOT ALWAYS WHAT IT SEEMS. REVNEC [Internet]. 2017Aug.22 [cited 2024Jul.17];22(1):25-9. Available from: https://revistas.rcaap.pt/nascercrescer/article/view/12895



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