Case of primary mucosa associated lymphoid tissue lymphoma of the lacrimal sac.

Abstract

Introduction: Primary lacrimal sac lymphoid tumors are a rare entity, the most frequent being the diffuse large B cell lymphoma and the extranodal marginal zone B cell lymphoma of mucosa associated lymphoid tissue (MALT lymphoma). We report a case of primary lacrimal sac lymphoma treated primarily with conformal radiotherapy.

Case report: An 86 years-old female presents with a symptomatic mass on the right lacrimal fossa area. Clinical investigation with orbital CT scan, Doppler ultra-sonography, incisional biopsy and systemic investigation lead to the diagnosis of a MALT lymphoma, Ann Harbour stage IE. Primary small dose three dimensional conformal radiotherapy was performed, with complete remission of the local lesion. No signs of recurrence were identified on follow-up.

Discussion: Primary MALT lymphoma of the lacrimal sac is a rare entity and its presentation may be misleading. Radiotherapy may be considered as primary treatment in local lesions.