Two for One! Epiphenomenon of Multiple Evanescent White Dot Syndrome: A Case Report

Authors

  • Telma Machado Ophthalmology Department, Hospitais da Universidade de Coimbra, Unidade Local de Saúde de Coimbra, Coimbra, Portugal; Clinical Academic Center of Coimbra, Hospital Pediátrico de Coimbra, Unidade Local de Saúde de Coimbra, Coimbra, Portugal https://orcid.org/0009-0001-0727-4886
  • Cristina Fonseca Ophthalmology Department, Hospitais da Universidade de Coimbra, Unidade Local de Saúde de Coimbra, Coimbra, Portugal; Clinical Academic Center of Coimbra, Hospital Pediátrico de Coimbra, Unidade Local de Saúde de Coimbra, Coimbra, Portugal https://orcid.org/0000-0001-8039-9418

DOI:

https://doi.org/10.48560/rspo.33248

Keywords:

Choroidal Neovascularization, Multifocal Choroiditis, White Dot Syndromes

Abstract

We present a case of a 24-year-old female with unilateral subacute visual loss (20/40 OD and 20/16 OS) and metamorphopsias for one week. Examination of the right eye revealed multiple white dots involving the posterior pole and mid periphery, an old chorioretinal scar in the inferior vascular arcade, and atrophic punched-out lesions in the inferior periphery. Optical coherence tomography showed choroidal neovascularization (CNV) arising from the superior border of the main scar. The patient was diagnosed with secondary multiple evanescent white dot syndrome (MEWDS) complicated by CNV, in the presence of a quiescent multifocal choroiditis (MFC). She was treated with anti-VEGF injection and corticosteroids. Two months later, vision improved to 20/20 OD, the white spots faded and CNV regressed. Secondary MEWDS seems to be an epiphenomenon that occurs by triggered inflammation of the outer retina and is associated with MFC. Multimodal imaging improves the diagnosis of the spectrum of MEWDS.

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References

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Published

2024-09-28

How to Cite

Machado, T., & Fonseca, C. (2024). Two for One! Epiphenomenon of Multiple Evanescent White Dot Syndrome: A Case Report. Revista Sociedade Portuguesa De Oftalmologia, 48(3), 233–236. https://doi.org/10.48560/rspo.33248

Issue

Section

Case Reports