Type I Uveal Effusion Syndrome: a Case Report

Abstract

Introduction: Uveal effusion syndrome (UES) is a rare idiopathic serous detachment of the retina, most probably caused by scleral abnormality. Treatment may be challenging due to the frequent relapsing course and unresponsiveness of the disease. The authors report a case of a type I bilateral UES, successfully resolved with surgery.

Methods: The authors report a case of a 61-year-old man with a history of high bilateral hyperopia since childhood and nanophthalmic eyes. On examination bilateral exudative retinal detachment was evident.

Results: Patient was treated medically and since there was no clinical response, underwent bilateral inferonasal and inferotemporal scleral flaps and full-thicknes sclerectomy. Thirty months after the first surgery on the right eye and six months after surgery on the left eye, patient had a visual acuity of 20/100 and resolution of the retinal detachment on both eyes.

Conclusion: The case reported highlights the importance of surgical approach in some cases of UES, which are frequently refractory to medical therapy. Surgical intervention aimed to decrease the overall resistance to choroidal fluid outflow, facilitating drainage  and resolution of retinal detachment.