Abdominal Pain in a Female Adolescent: A Diagnosis to Consider

Abstract

OHVIRA syndrome is a rare congenital female anomaly, characterized by the triad: uterus didelphys, unilaterally obstructed hemivagina and ipsilateral renal agenesis. The authors   present a case of a 12-year-old girl with cyclic abdominal pain, scarce catamenia and intense dysmenorrhea refractory to NSAIDs. An abdominal and pelvic computized tomography was carried out which revealed renal agenesis, duplication of the uterus, cervix, and vagina, and hematocolpos, suggesting vaginal obstruction. The prompt treatment allows a clear improvement in the clinical and reproductive prognosis, so the authors emphasize the importance of the knowledge and suspicion of this condition, allowing the diagnosis, referral, and early approach.