Massive hemorrhage in patient with Klippel-Trenaunay-Weber syndrome

Authors

  • João Colaço Serviço de Anestesiologia, Hospital de Faro
  • Angela Garcia Alves Chefe de Serviço de Anestesiologia – Centro Hospitalar Lisboa Norte
  • Helena Gomes Santos Assistente Hospitalar Graduada - Centro Hospitalar Lisboa Norte

DOI:

https://doi.org/10.25751/rspa.8845

Keywords:

Klippel-Trenaunay-Weber syndrome, Massive hemorrhage, angiodysplasia, aneurysmectomy, femoral-popliteal bypass surgery, coagulopathy, introperative Cell-Saver

Abstract

Klippel Trenaunay Weber syndrome (SKTW) is rare congenital disease characterized by cutaneous hemangioma, bone and soft tissue hypertrophy and venous/lymphatic abnormalities related with arterio-venous malformations and coagulopathy. 

There are about 1000 case reports found in the literature, of which only 12 include anesthetic approach. 

The authors report a case of a patient diagnosed with SKTW submitted to a right superficial femoral artery aneurysmectomy and femoral-popliteal bypass surgery, under general anesthesia complicated with massive hemorrhage (total blood loss of 8050mL against 500-1000mL estimated for this kind of procedure), due to angiodisplasia of right leg.

The authors discuss an aggressive approach to massive blood loss, mainly regarding the use of  introperative Cell-Saver and fluid rapid infusers (Level 1 ®).

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Published

2016-03-22

How to Cite

Colaço, J., Alves, A. G., & Santos, H. G. (2016). Massive hemorrhage in patient with Klippel-Trenaunay-Weber syndrome. Journal of the Portuguese Society of Anesthesiology, 21(1), 16–19. https://doi.org/10.25751/rspa.8845

Issue

Vol. 21 No. 1 (2012): Journal of the Portuguese Society of Anesthesiology

Section

Case Report

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