Kawasaki disease and cardiovascular complications in pediatrics


  • Marlene Rodrigues Departament of Pediatrics, Hospital de Braga
  • Joana Cunha de Oliveira Departament of Pediatrics, Hospital de Braga
  • Fábia Carvalho Departament of Pediatrics, Hospital de Braga
  • Helena Silva Departament of Pediatrics, Hospital de Braga
  • Carla Moreira Departament of Pediatrics, Hospital de Braga
  • Sofia Granja Departament of Pediatrics Cardiology, Hospital de Braga
  • Augusta Gonçalves Departament of Pediatrics, Hospital de Braga




Coronary aneurysms, Kawasaki disease, vasculitis


Introduction: Kawasaki disease (KD) is a systemic vasculitis of unknown etiology, which is the main cause of acquired heart disease in children in developed countries. It´s rare before six months of age and the main complications result from the development of coronary ectasia or aneurysms which can lead to ischemic heart disease.
Case report: We present a two-months-old child with diagnosis of incomplete KD, at the day eighth of fever, refractory to treatment with the first dose of immunoglobulin and aspirin. Echocardiographic evaluation performed in the acute phase showed diffuse ectasia of coronary arteries and perivascular brightness, with no other changes. He was treated with second dose of imunoglubulin and acetylsalicylic acid, with clinical improvement.
Conclusion: This clinical case report highlights the importance of early diagnosis and treatment of KD, as well as subsequent follow-up, bearing in mind the potential late cardiovascular complications of this pediatric disease.


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How to Cite

Rodrigues M, de Oliveira JC, Carvalho F, Silva H, Moreira C, Granja S, Gonçalves A. Kawasaki disease and cardiovascular complications in pediatrics. REVNEC [Internet]. 2018Apr.13 [cited 2024Apr.14];27(1):54-8. Available from: https://revistas.rcaap.pt/nascercrescer/article/view/10192



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