Regressão da linguagem com manifestação de epilepsia
DOI:
https://doi.org/10.25753/BirthGrowthMJ.v30.i2.17501Palavras-chave:
cognição, epilepsia, síndromes epiléticos, síndrome de Landau-KleffnerResumo
Introdução: As encefalopatias epiléticas são um conjunto de síndromes dependentes da idade, em que a atividade paroxística ictal e interictal é responsável por deterioração cognitiva e neuropsicológica.
Caso Clínico: Um rapaz de quatro anos de idade, previamente saudável, foi admitido no Serviço de Urgência devido a um quadro de regressão da linguagem compreensiva e expressiva com quatro dias de evolução, associado ao surgimento de crises epiléticas. As características clínicas e alterações no eletroencefalograma conduziram ao diagnóstico de síndrome de Landau-Keffner. O rapaz foi tratado com valproato, clobazam e prednisolona, com melhoria da linguagem.
Discussão/Conclusão: A síndrome de Landau-Kleffner é uma encefalopatia epilética rara, caracterizada por afasia adquirida, epilepsia e anomalias paroxísticas eletroencefalográficas. Deve haver suspeita clínica perante uma criança com desenvolvimento normal que inicia um quadro de regressão da linguagem. O diagnóstico precoce e tratamento adequado são importantes para melhorar o prognóstico.
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Direitos de Autor (c) 2021 Joana Ferreira, Sofia Lopes, José Carmona Lopes, Cristina Ferreira, Catarina Magalhães
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